RESUMO
Biliary atresia (BA) is classically described at the neonatal age. However, rare cases of BA in older infants have also been reported. We report four cases of late-onset BA in infants older than 4 weeks (3 males, 1 female), and describe the diagnostic and management difficulties. One of the cases had a late-onset (29 weeks) presentation with a successful surgical procedure. We highlight the importance of this unusual differential diagnosis in infants with cholestatic syndrome, who may benefit from Kasai surgery, regardless of age.
Assuntos
Humanos , Masculino , Feminino , Lactente , Atresia Biliar/diagnóstico , Transtornos de Início Tardio/diagnóstico , Fígado/patologia , Atresia Biliar/patologia , Atresia Biliar/cirurgia , Biópsia , Diagnóstico Diferencial , Artéria Hepática/patologia , Transtornos de Início Tardio/patologia , Transtornos de Início Tardio/cirurgiaRESUMO
Biliary atresia (BA) is classically described at the neonatal age. However, rare cases of BA in older infants have also been reported. We report four cases of late-onset BA in infants older than 4 weeks (3 males, 1 female), and describe the diagnostic and management difficulties. One of the cases had a late-onset (29 weeks) presentation with a successful surgical procedure. We highlight the importance of this unusual differential diagnosis in infants with cholestatic syndrome, who may benefit from Kasai surgery, regardless of age.